Bordeianou Liliana, Ryan Daniel P, Goldstein Allan M
Department of Pediatric Surgery, Massachusetts General Hospital, Warren 1153, Boston, MA 02114, USA.
Pediatr Surg Int. 2005 Sep;21(9):742-4. doi: 10.1007/s00383-005-1469-7. Epub 2005 Oct 20.
Beckwith-Wiedemann Syndrome (BWS) is associated with somatic overgrowth and a high risk for embryonal tumors, including hepatoblastoma, a highly malignant liver tumor of childhood. Focal nodular hyperplasia (FNH), on the other hand, is a benign tumor of the liver that is uncommon in childhood. Herein we describe a case of FNH in a child with BWS, the first such report in the literature.
贝克威思-维德曼综合征（BWS）与身体过度生长以及胚胎性肿瘤的高风险相关，这些肿瘤包括肝母细胞瘤，一种儿童期高度恶性的肝脏肿瘤。另一方面，局灶性结节性增生（FNH）是一种肝脏良性肿瘤，在儿童期并不常见。在此我们描述了一例患有BWS的儿童发生FNH的病例，这是文献中的首例此类报告。
