Mercuri Sandro, Gazzeri Roberto, Galarza Marcelo, Esposito Stefano, Giordano Marco
Dipartimento di scienze Neurologiche - Neurochirurgia, Rome, Italy.
J Neurooncol. 2005 Jun;73(2):169-72. doi: 10.1007/s11060-004-4595-5.
Intracranial pheochromocytomas are extremely rare tumors. Reported cases include metastatic tumors without known cases of primary pheochromocytomas.
A female patient with a history of a surgically treated adrenal pheochromocytoma presented 23 years later with headache, nausea and blood hypertension. A head CT scan demonstrated a right temporoparietal meningeal heterogeneous lesion with a surrounding hyperdense ring. No other lesions were disclosed.
The lesion developed in the inner and outer surface of the dura without brain infiltration and it was totally resected. The patient is free of disease 6 years after brain surgery.
To our knowledge this is the first reported case of a primary meningeal pheochromocytoma.
颅内嗜铬细胞瘤是极其罕见的肿瘤。报道的病例包括转移性肿瘤,尚无原发性嗜铬细胞瘤的已知病例。
一名有肾上腺嗜铬细胞瘤手术治疗史的女性患者,23年后出现头痛、恶心和高血压。头部CT扫描显示右侧颞顶叶脑膜有一不均匀病变,周围有高密度环。未发现其他病变。
病变发生于硬脑膜内外表面,未侵犯脑实质,予以完整切除。脑手术后6年患者无疾病复发。
据我们所知,这是首例原发性脑膜嗜铬细胞瘤的报道病例。