肺泡蛋白沉积症与终末期肺纤维化：一种罕见的关联。

Pulmonary alveolar proteinosis and end-stage pulmonary fibrosis: a rare association.

作者信息

Agarwal Prachi P, Seely Jean M, Perkins D Garth, Matzinger Fred R, Alikhan Qasim

机构信息

Department of Diagnostic Imaging, The Ottawa Hospital, Ottawa, Ontario, Canada.

出版信息

J Thorac Imaging. 2005 Aug;20(3):242-4. doi: 10.1097/01.rti.0000160733.74997.2d.

DOI:10.1097/01.rti.0000160733.74997.2d

PMID:16077345

Abstract

We present the high resolution CT features of marked pulmonary fibrosis in a patient known to have pulmonary alveolar proteinosis (PAP) confirmed on open lung biopsy. Significant fibrosis in PAP is an extremely rare occurrence with only a few case reports. Our case demonstrated a predominantly central distribution, which has not been described previously.

摘要

我们展示了一名经开胸肺活检确诊为肺泡蛋白沉积症（PAP）患者显著肺纤维化的高分辨率CT特征。PAP中出现显著纤维化极为罕见，仅有少数病例报告。我们的病例显示主要为中央分布，这在之前未曾有过描述。