Haim M, Holm N V, Rosenberg T
National Eye Clinic for the Visually Impaired, Copenhagen.
Acta Ophthalmol (Copenh). 1992 Apr;70(2):178-86. doi: 10.1111/j.1755-3768.1992.tb04121.x.
In a nation-wide study we utilized all available sources to characterize the prevalence rates of retinitis pigmentosa. 1301 persons, 715 males and 586 females, were identified, with a diagnosis of retinitis pigmentosa or some other tapetoretinal dystrophy, and living in Denmark per January 1, 1988. The corresponding completeness corrected prevalence rate of retinitis pigmentosa was 1:3026. All cases were classified as 'certain', 'probable', or 'possible'. The age specific prevalence rates increased until 40-50 years, reaching a level of 35-40 male cases per 100,000 and 25-30 female cases per 100,000. Age specific prevalence rates were standardized to the WHO World Standard Population and compared to rates reported from Britain and The United States. World standardized prevalence rate for males was 25.29 per 100,000 and for females 19.31 per 100,000. The preponderance of males was highly statistically significant, (P less than 0.01).
在一项全国性研究中，我们利用所有可用资源来确定色素性视网膜炎的患病率。我们确定了1301人，其中男性715人，女性586人，他们被诊断患有色素性视网膜炎或其他一些视网膜色素变性疾病，并且在1988年1月1日居住在丹麦。色素性视网膜炎相应的校正后完备患病率为1:3026。所有病例被分为“确定”、“可能”或“疑似”。年龄别患病率在40至50岁之前呈上升趋势，男性达到每10万人中有35至40例，女性为每10万人中有25至30例。年龄别患病率根据世界卫生组织的世界标准人口进行标准化，并与英国和美国报告的患病率进行比较。男性的世界标准化患病率为每10万人中有25.29例，女性为每10万人中有19.31例。男性患病率的优势具有高度统计学意义（P<0.01）。
