因克-特综合征的泌尿生殖系统表现导致的危及生命的严重血尿。
Life-threatening gross hematuria due to genitourinary manifestation of Klippel-Trenaunay syndrome.
作者信息
Rubenwolf Peter, Roosen Alexander, Gerharz Elmar W, Kirchhoff-Moradpour Antje, Darge Kassa, Riedmiller Hubertus
机构信息
Department of Urology, Julius-Maximilians-University Medical School, Würzburg, Germany.
出版信息
Int Urol Nephrol. 2006;38(1):137-40. doi: 10.1007/s11255-005-3154-0.
The Klippel-Trenaunay Syndrome (KTS) is defined as a triad of cutaneous capillary malformations, venous varicosities, bone and soft tissue hemi-hypertrophy. The urinary tract is involved in up to 10%. We report the clinical presentation and surgical management of a 9-year-old boy with extensive lympho-venous malformations of the bladder which led to massive recurrent gross hematuria.
克-特综合征（KTS）的定义为皮肤毛细血管畸形、静脉迂曲扩张、骨骼和软组织半侧肥大三联征。尿路受累发生率高达10%。我们报告了一名9岁男孩的临床表现及手术治疗情况，该男孩患有广泛的膀胱淋巴静脉畸形，导致大量反复肉眼血尿。
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