Lei Hongen, Guan Xing, Han Hu, Qian Xiaosong, Zhou Xiaoguang, Zhang Xiaodong, Tian Long
Department of Urology, Beijing Chao-Yang Hospital, Capital Medical University, Beijing, China.
Department of Urology, Beijing Chao-Yang Hospital, Capital Medical University, Beijing, China.
Sex Med. 2018 Jun;6(2):180-183. doi: 10.1016/j.esxm.2017.12.001. Epub 2018 Feb 13.
Klippel-Trenaunay syndrome (KTS) is a rare congenital vascular disorder characterized by a triad of cutaneous port wine capillary malformations, varicose veins, and hemihypertrophy of bone and soft tissues.
To report on a rare case of KTS in an adult man manifested by painless urethral bleeding during penile erection briefly review the clinical presentation and management of the genitourinary forms of this syndrome.
On presentation, the clinical features of this patient, including medical history, signs and symptoms, and imaging examinations, were recorded. After diagnosis and initial treatment, a literature review of the urethral features of KTS was performed and is discussed in this report.
A 35-year-old man with KTS presented with painless urethral bleeding during penile erection that was associated with posterior urethral vascular malformations. The coagulation method was used to treat the malformation, and no urethral bleeding or gross hematuria occurred during a postoperative follow-up period of 6 months.
This case demonstrates that coagulation therapy and careful follow-up can be adequate treatment approaches for urethral features of KTS. However, the long-term efficacy of coagulation for this disorder should be investigated further. Lei H, Guan X, Han H, et al. Painless Urethral Bleeding During Penile Erection in an Adult Man With Klippel-Trenaunay Syndrome: A Case Report. Sex Med 2018;6:180-183.
克-特综合征（KTS）是一种罕见的先天性血管疾病，其特征为皮肤葡萄酒色斑状毛细血管畸形、静脉曲张以及骨骼和软组织半侧肥大三联征。
报告一例成年男性克-特综合征罕见病例，其表现为阴茎勃起时无痛性尿道出血，并简要回顾该综合征泌尿生殖系统表现的临床特征及治疗方法。
记录该患者的临床表现，包括病史、体征和症状以及影像学检查结果。在诊断和初步治疗后，对克-特综合征的尿道特征进行文献回顾并在本报告中进行讨论。
一名35岁克-特综合征男性患者出现阴茎勃起时无痛性尿道出血，这与后尿道血管畸形有关。采用凝固法治疗该畸形，术后6个月随访期间未出现尿道出血或肉眼血尿。
该病例表明，凝固疗法和仔细随访可能是治疗克-特综合征尿道表现的适当方法。然而，凝固疗法对该疾病的长期疗效仍需进一步研究。雷H，关X，韩H等。成年男性克-特综合征患者阴茎勃起时无痛性尿道出血：一例报告。性医学2018；6：180 - 183。
