Mehta M V, Porecha Mehul M, Mehta Purvi J
Department of Surgery and Anesthesiology, M P Shah medical college, G G Hospital, Jamnagar.
Indian J Gastroenterol. 2006 Jan-Feb;25(1):38-9.
Peutz-Jeghers syndrome (PJS) is characterized by intestinal hamartomatous polyposis (usually affecting the jejunum) and mucocutaneous melanin spots. Though malignant changes are not common, PJS can predispose to carcinoma in the GI tract and elsewhere. We report a 25-year-old man with PJS who developed small intestinal adenocarcinoma and presented with small bowel obstruction due to jejuno-ileal intussusception.
佩-吉二氏综合征(PJS)的特征为肠道错构瘤性息肉病(通常累及空肠)和黏膜皮肤黑色素斑。虽然恶性变并不常见,但PJS可使胃肠道及其他部位发生癌变的风险增加。我们报告一例25岁患有PJS的男性患者,该患者发生了小肠腺癌,并因空肠-回肠套叠出现小肠梗阻。