Weeks J K, Helton K J, Conley M E, Onciu M, Khan R B
Department of Radiological Sciences, St Jude Children's Research Hospital, Memphis, TN 38105-3300, USA.
AJNR Am J Neuroradiol. 2006 Apr;27(4):884-6.
We report a patient with X-linked lymphoproliferative disease (XLP) who developed multiple central nervous system (CNS) manifestations of Epstein-Barr virus infection. XLP, or Duncan syndrome, is a rare inherited disorder characterized by the inability to clear Epstein-Barr virus infection. In addition to Epstein-Barr virus encephalitis, CNS lymphoproliferative disease, and lymphoma, this patient also developed MR angiographic evidence of diffuse fusiform aneurysmal dilation of intracranial vessels.
我们报告了一名患有X连锁淋巴增殖性疾病（XLP）的患者，该患者出现了爱泼斯坦-巴尔病毒感染的多种中枢神经系统（CNS）表现。XLP，即邓肯综合征，是一种罕见的遗传性疾病，其特征是无法清除爱泼斯坦-巴尔病毒感染。除了爱泼斯坦-巴尔病毒性脑炎、中枢神经系统淋巴增殖性疾病和淋巴瘤外，该患者还出现了颅内血管弥漫性梭形动脉瘤样扩张的磁共振血管造影证据。
