Wat Christina S K, Yuen Hunter K L, Tse K K, Lam Dennis S C, Chan Nongnart
Department of Ophthalmology and Visual Sciences, The Chinese University of Hong Kong, Hong Kong Eye Hospital, Kowloon, Hong Kong SAR, People's Republic of China.
Ophthalmic Plast Reconstr Surg. 2006 May-Jun;22(3):216-8. doi: 10.1097/01.iop.0000217567.90717.52.
Langerhans cell histiocytosis is a disorder characterized by the proliferation of histiocytes of the mononuclear phagocyte system. Cutaneous Langerhans cell histiocytosis can develop as a solitary lesion or more frequently as part of a multisystem disease. This report describes a case of cutaneous Langerhans cell histiocytosis affecting the eyelids, resulting in a coloboma-like defect. The clinical features and management are discussed.
朗格汉斯细胞组织细胞增多症是一种以单核吞噬细胞系统组织细胞增殖为特征的疾病。皮肤朗格汉斯细胞组织细胞增多症可表现为孤立性病变，或更常见地作为多系统疾病的一部分出现。本报告描述了一例累及眼睑的皮肤朗格汉斯细胞组织细胞增多症病例，导致类似睑裂缺损的缺陷。并对其临床特征及治疗进行了讨论。
