Jastrzebski Marek, Bacior Bogumila, Dimitrow Pawel Petkow, Kawecka-Jaszcz Kalina
Cardiac Department, Jagiellonian University College of Medicine, ul. Kopernika 17, 31-501 Krakow, Poland.
Europace. 2006 Dec;8(12):1045-7. doi: 10.1093/europace/eul121. Epub 2006 Nov 10.
A short PQ interval is a common finding in patients with Fabry disease. However, there have been few electrophysiological studies in Fabry disease, and it is not clear whether the short PQ interval that is present in this disease results from preexcitation or enhanced atrioventricular nodal conduction. We present a case of a 43-year-old man with syncope, sick sinus syndrome, a PQ interval of 80 ms, and palpitations. Electrophysiological study showed PA, AH, and HV intervals of 24, 32, and 34 ms, respectively, and features of enhanced atrioventricular nodal conduction. The presence of an atrioventricular accessory pathway was excluded. We conclude that the short PQ interval in Fabry disease can result from accelerated conduction in the atrioventricular node.
PQ间期缩短在法布里病患者中很常见。然而，针对法布里病的电生理研究较少，目前尚不清楚该病中出现的短PQ间期是由预激还是房室结传导增强所致。我们报告一例43岁男性患者，有晕厥、病态窦房结综合征、PQ间期80毫秒及心悸症状。电生理研究显示，PA间期、AH间期和HV间期分别为24毫秒、32毫秒和34毫秒，具有房室结传导增强的特征。排除了房室旁路的存在。我们得出结论，法布里病中的短PQ间期可能是由房室结传导加速导致的。
