Vercueil L
EFSN, CHU de Grenoble, 38043 Grenoble, France.
Neurophysiol Clin. 2006 Sep-Dec;36(5-6):327-31. doi: 10.1016/j.neucli.2006.12.002. Epub 2007 Jan 19.
Myoclonus is a movement disorder characterized by the occurrence of an involuntary abrupt muscle contraction causing a sudden unexpected jerk. Many other movement disorders can present with the same jerky, shock-like appearance. This paper reviews the clinical and neurophysiologic arguments supporting the distinction between true myoclonus and various imitators, including chorea, ballism, tics, dystonia, stereotypy, tremor and restless limbs. To be differentiated from myoclonus, these movement disorders, despite their heterogeneity, are distinctive through the patterned profile of muscle activation, the longer duration of the muscle contraction, the conditions in which they occur, and their suppressibility at will.
肌阵挛是一种运动障碍,其特征是出现不自主的突然肌肉收缩,导致突然意外的抽搐。许多其他运动障碍也可能呈现出相同的急促、类似电击的表现。本文回顾了支持区分真性肌阵挛与各种模仿性疾病(包括舞蹈症、投掷症、抽搐、肌张力障碍、刻板动作、震颤和不宁腿)的临床和神经生理学依据。尽管这些运动障碍具有异质性,但要与肌阵挛区分开来,可通过肌肉激活的模式特征、肌肉收缩的持续时间更长、发生的条件以及它们是否可随意抑制来进行鉴别。