Watts Adam C, Ballantyne J Andrew, Fraser Maria, Simpson A Hamish R W, Porter Daniel E
Edinburgh University Department of Orthopaedic Surgery, New Royal Infirmary, Little France, Edinburgh, UK.
J Hand Surg Am. 2007 May-Jun;32(5):667-73. doi: 10.1016/j.jhsa.2007.02.008.
To determine the relationship between the length of the ulna as a proportion of height (proportional ulnar length [PUL]), forearm and wrist ranges of motion, and degree of observable deformity in people with hereditary multiple exostoses.
One hundred forty-two people with hereditary multiple exostoses were examined; 35 were under the age of 15 years and therefore were presumed to be skeletally immature. Elbow, forearm, and wrist motion were measured, and the radius and ulna were palpated for osteochondromas. Ulnar length was estimated as a proportion of height (PUL) in skeletally immature subjects. The relationships between total active motion, number of palpable osteochondromas, and proportional length were examined for one randomly selected limb from each subject.
A negative correlation was found between the number of palpable osteochondromas and range of forearm rotation. The degree of forearm motion in those under the age of 15 years was directly related to PUL and indirectly related to the number of palpable osteochondromas. Children whose PUL is within the normal range have a normal range of motion.
In a child with hereditary multiple exostoses affecting the forearm, the PUL is associated with the range of movement and deformity, and it can be a useful adjunct in deciding the appropriate management.
确定遗传性多发性骨软骨瘤患者尺骨长度占身高的比例(比例尺骨长度[PUL])、前臂和腕关节活动范围以及可观察到的畸形程度之间的关系。
对142例遗传性多发性骨软骨瘤患者进行检查;其中35例年龄在15岁以下,因此被认为骨骼未成熟。测量肘、前臂和腕关节的活动度,并触诊桡骨和尺骨有无骨软骨瘤。对于骨骼未成熟的受试者,以尺骨长度占身高的比例(PUL)来估算尺骨长度。从每个受试者中随机选择一个肢体,检查其总主动活动度、可触及骨软骨瘤的数量与比例长度之间的关系。
可触及骨软骨瘤的数量与前臂旋转范围之间呈负相关。15岁以下患者的前臂活动度与PUL直接相关,与可触及骨软骨瘤的数量间接相关。PUL在正常范围内的儿童,其活动度正常。
在患有影响前臂的遗传性多发性骨软骨瘤的儿童中,PUL与活动范围和畸形有关,它可以作为决定适当治疗方法的有用辅助指标。