Wojas-Pelc Anna, Wielowieyska-Szybińska Dorota
Katedra i Klinika Dermatologii, Collegium Medicum, Uniwersytetu Jagiellońskiego, Kraków.
Przegl Lek. 2007;64(6):438-41.
Skin scleroderma (LS) is characterised by stiffness of skin and/or deeper tissues. As opposed to systemic scleroderma, the involvement of internal organs and Raynaud phenomenon are predominately not observed in morphea. LS is quite rare disease, more frequent in women and young people. There are several useful classifications of skin scleroderma in literature, however the classification which concerns the shape and extension of LS lesion and depth of stiffness is concerned to be the most clear. LS is divided into: plaque morphoea, generalised morphoea, blistering morphoea, linear morphoea and deep morphoea. Different types of skin scleroderma lesions can be observed in one patient or can combine linear and deep fibrosis. Presented classification is clinically useful and it has prognostic and therapeutic implications.
局限性硬皮病(LS)的特征是皮肤和/或深层组织僵硬。与系统性硬皮病不同,硬斑病中主要不会出现内脏器官受累和雷诺现象。LS是一种相当罕见的疾病,在女性和年轻人中更为常见。文献中有几种有用的皮肤硬皮病分类方法,然而,涉及LS病变的形状、范围和僵硬深度的分类被认为是最清晰的。LS分为:斑块状硬斑病、泛发性硬斑病、大疱性硬斑病、线状硬斑病和深部硬斑病。在一名患者身上可以观察到不同类型的皮肤硬皮病病变,或者可以合并线状和深部纤维化。所提出的分类在临床上是有用的,并且具有预后和治疗意义。