Ahmad Zubair, Nisa Azizun, Idrees Romana, Minhas Khurram, Pervez Shahid, Mumtaz Khalid
Department of Pathology and Microbiology, Aga Khan University Hospital, Karachi, Pakistan.
J Coll Physicians Surg Pak. 2008 Jan;18(1):50-2.
Hepatic angiosarcomas are rare tumours with poor prognosis, with patients usually dying within 6 months. Metastases mainly occur in lymph nodes, spleen, lungs, bones and adrenals. Metastasis to small intestine is even rarer. Similarly, primary or metastatic angiosarcomas in small intestine are extremely rare, often present with recurrent gastrointestinal bleeding and anemia, and have an extremely poor prognosis. Both primary or metastatic intestinal angiosarcomas may exhibit epithelioid morphology. It may be very difficult to differentiate between primary and secondary cases in intestine and especially when the tumour exhibits epithelioid morphology.
肝血管肉瘤是一种预后较差的罕见肿瘤,患者通常在6个月内死亡。转移主要发生在淋巴结、脾脏、肺、骨骼和肾上腺。转移至小肠的情况更为罕见。同样,小肠原发性或转移性血管肉瘤极其罕见,常表现为反复胃肠道出血和贫血,预后极差。原发性或转移性肠道血管肉瘤均可表现为上皮样形态。在肠道中区分原发性和继发性病例可能非常困难,尤其是当肿瘤表现为上皮样形态时。