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Corticosteroid-responsive dominantly inherited neuropathy in childhood.

作者信息

Bird S J, Sladky J T

机构信息

Department of Neurology, University of Pennsylvania School of Medicine, Philadelphia.

出版信息

Neurology. 1991 Mar;41(3):437-9. doi: 10.1212/wnl.41.3.437.

DOI:10.1212/wnl.41.3.437
PMID:1848688
Abstract

We describe three children with corticosteroid-responsive inflammatory demyelinating polyneuropathy from families with dominantly inherited neuropathy. There were atypical clinical, electrophysiologic, and pathologic characteristics that suggested a coexistent inflammatory demyelinating neuropathy and that should alert the clinician to the possibility of an associated acquired, potentially treatable disorder.

摘要

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