McBrien Angela, Paterson Annie, Gladstone Dennis, Craig Brian
Department of Paediatric Cardiology, The Royal Belfast Hospital for Sick Children, 180 Falls Road, Belfast, Northern Ireland, UK.
Pediatr Cardiol. 2008 Sep;29(5):1011-3. doi: 10.1007/s00246-008-9251-y. Epub 2008 Jul 2.
This is the second reported case of coarctation in a right aortic arch with an aberrant left brachiocephalic artery. In this patient, the right subclavian artery is aneurysmal, making this case unique. There is a pressure gradient of 34 mm Hg between ascending and descending aorta. Both the conventional and computed tomography angiographic images are presented. This is the first reported case to include imaging of this anatomy prior to surgery. It is also the first report of primary surgical management following a correct initial diagnosis.
这是第二例报告的右位主动脉弓伴迷走左头臂动脉合并缩窄的病例。在该患者中，右锁骨下动脉呈瘤样扩张，使得此病例具有独特性。升主动脉和降主动脉之间存在34 mmHg的压力阶差。文中展示了传统血管造影图像和计算机断层扫描血管造影图像。这是首例报告的在手术前对该解剖结构进行成像的病例。这也是首例在初始诊断正确后进行一期手术治疗的报告。
