Park Dong-Hyuk, Kang Shin-Hyuk, Lim Dong-Jun, Kwon Taek-Hyun, Park Jung-Yul, Chung Yong-Gu, Lee Hoon-Kap
Department of Neurosurgery, Korea University Medical Center, Korea University College of Medicine, Seoul, Korea.
Pediatr Neurosurg. 2008;44(6):486-9. doi: 10.1159/000180304. Epub 2008 Dec 10.
A rare case involving multiple intracranial aneurysms with intraventricular hemorrhage (IVH) in a child, accompanied by unilateral fibromuscular dysplasia (FMD) of the renal artery, is reported. A 12-year-old girl presented with secondary hypertension and fourth-ventricle IVH. Cerebral angiography showed multiple aneurysms in the anterior communicating artery, right posterior cerebral artery, and right superior cerebellar artery. Abdominal angiography revealed marked stenosis and dilatation of the left renal artery. Coil embolization of the intracranial aneurysms was successfully performed. Then, a left nephrectomy and autotransplantation were performed. At the time of discharge, she was in an almost normal neurological condition. The association between renal artery FMD and aneurysmal rupture is extremely rare. This case is the first report of multiple intracranial aneurysms with IVH treated successfully with coils in a child concomitant with FMD of the renal artery.
报告了一例罕见病例，患儿患有多发性颅内动脉瘤并伴有脑室内出血（IVH），同时伴有肾动脉单侧纤维肌性发育不良（FMD）。一名12岁女孩出现继发性高血压和第四脑室IVH。脑血管造影显示前交通动脉、右侧大脑后动脉和右侧小脑上动脉存在多个动脉瘤。腹部血管造影显示左肾动脉明显狭窄和扩张。成功实施了颅内动脉瘤的弹簧圈栓塞术。随后，进行了左肾切除术和自体肾移植术。出院时，她的神经状况几乎正常。肾动脉FMD与动脉瘤破裂之间的关联极为罕见。该病例是首例关于伴有肾动脉FMD的儿童多发性颅内动脉瘤合并IVH经弹簧圈成功治疗的报告。
