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与脑干脑炎相关的伏格特-小柳-原田病

Vogt-Koyanagi-Harada disease associated with brainstem encephalitis.

作者信息

Hashimoto Takao, Takizawa Hotake, Yukimura Kimie, Ohta Kouichi

机构信息

Department of Neurology, Aizawa Hospital, 2-5-1 Honjo, Matsumoto 390-8510, Japan.

出版信息

J Clin Neurosci. 2009 Apr;16(4):593-5. doi: 10.1016/j.jocn.2008.05.029. Epub 2009 Feb 6.

Abstract

We report on a 28-year-old man with a 2-year history of Vogt-Koyanagi-Harada disease (VKH), who developed one-and-a-half syndrome, facial hypoesthesia, facial nerve palsy, hearing loss and limb ataxia on the right side. An MRI showed inflammatory lesions in the pons extending into the left middle cerebellar peduncle. Corticosteroid treatment successfully ameliorated his symptoms and lesions. This patient demonstrated the possible association of brainstem encephalitis with VKH.

摘要

我们报告了一名28岁男性,患有伏格特-小柳-原田病(VKH)2年,出现了右侧的一个半综合征、面部感觉减退、面神经麻痹、听力丧失和肢体共济失调。磁共振成像(MRI)显示脑桥有炎症性病变并延伸至左侧小脑中脚。皮质类固醇治疗成功改善了他的症状和病变。该患者证明了脑干脑炎与VKH之间可能存在关联。

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