Koumbourlis Anastassios C
Division of Pediatric Pulmonary Medicine, Schneider Children's Hospital, North Shore-Long Island Jewish Health System, Albert Einstein College of Medicine, Great Neck, NY 11021, USA.
Paediatr Respir Rev. 2009 Mar;10(1):3-6. doi: 10.1016/j.prrv.2008.12.002.
Pectus Excavatum is the most common congenital abnormality of the chest wall. In the majority of the cases the condition is idiopathic. Affected patients tend to have lung volumes that are mildly decreased but within the normal range and they are often associated with mild air-trapping. Many patients show evidence of lower airway obstruction. Exercise intolerance is the most common symptom associated with pectus excavatum, and it is now believed to be due to cardiovascular rather than pulmonary causes. The psychological effect of the deformity often exceeds its actual physical effect. Several surgical techniques are available for the repair of the deformity, although the need for it is still considered controversial by many. The current article provides an in depth review of the pathophysiology and clinical characteristics of pectus excavatum, as well as an overview of the treatment options in order to help the practitioners caring of affected patients in their evaluation.
漏斗胸是最常见的胸壁先天性异常。在大多数情况下,该病为特发性。受影响的患者肺容积往往轻度减小,但仍在正常范围内,且常伴有轻度气体潴留。许多患者有下气道阻塞的证据。运动不耐受是与漏斗胸相关的最常见症状,目前认为这是由心血管而非肺部原因所致。畸形的心理影响往往超过其实际的身体影响。虽然许多人仍认为漏斗胸修复手术的必要性存在争议,但有几种手术技术可用于修复该畸形。本文深入综述了漏斗胸的病理生理学和临床特征,以及治疗选择概述,以帮助护理受影响患者的从业者进行评估。