Dracon M, Noël C, Ramon P, Wallaert B, Tonnel A B, Gosselin B, Lelièvre G, Tacquet A
Clinique Néphrologique, Hôpital Calmette, Lille.
Nephrologie. 1991;12(3):139-41.
Relapsing polychondritis is a rare connective tissue disorder characterized by inflammation of cartilagenous structures such as ears, nose, joints, trachea and larynx. Renal disease is unusual. A 41 years old man presented with auricular chondritis, subacute renal failure and lung hemorrhage. A renal biopsy disclosed a diffuse proliferative glomerulonephritis with extensive crescents. Immunofluorescent studies suggested a GNRP type III so called "non immunologic disease". He was treated by prednisone and plasmapheresis with rapid disappearance of pulmonary hemorrhages and good renal functional improvement.
复发性多软骨炎是一种罕见的结缔组织疾病，其特征为耳部、鼻部、关节、气管和喉部等软骨结构的炎症。肾脏疾病较为少见。一名41岁男性出现耳软骨炎、亚急性肾衰竭和肺出血。肾活检显示弥漫性增生性肾小球肾炎伴广泛新月体形成。免疫荧光研究提示为III型抗肾小球基底膜病，即所谓的“非免疫性疾病”。他接受了泼尼松和血浆置换治疗，肺出血迅速消失，肾功能明显改善。
