Setor de Eletrocardiografia, Hospital de Base, Av. Faria Lima, 5544, 15090-000, São José do Rio Preto City, Brazil.
Cardiovasc Pathol. 2010 May-Jun;19(3):191-2. doi: 10.1016/j.carpath.2008.12.012. Epub 2009 Feb 20.
A 24-year-old-man had right-sided heart failure of 3 months' duration. A Doppler echocardiogram revealed atrium and right ventricular enlargement, obliteration of the right ventricular apex, and a mass with an echolucent center measuring 20x21 mm in the right ventricular outlet. He died of pulmonary embolism. At autopsy, a huge organized thrombus obliterating the right ventricular apex passing through the tricuspid valve to the right atrium and then extending to the inferior vena cava up to the suprahepatic veins was seen. Histologically, an intense fibrotic thickening of the endomyocardium extending into the myocardium was observed. Cardiac thrombosis associated with endomyocardial fibrosis should be added to the list of causes of Budd-Chiari syndrome.
一名 24 岁男性患有 3 个月的右侧心力衰竭。多普勒超声心动图显示右心房和右心室扩大,右心室心尖闭塞,以及在右心室流出道处有一个回声透明中心的 20x21 毫米的肿块。他死于肺栓塞。尸检时,可见一个巨大的机化血栓阻塞右心室心尖,穿过三尖瓣进入右心房,然后延伸至下腔静脉至肝上腔静脉。组织学上,观察到心内膜的强烈纤维化增厚延伸到心肌。与心内膜心肌纤维化相关的心脏血栓应添加到布加综合征的病因列表中。