Theodossi A, Al-Ashbal A A, Dische F E, Pryor J S, Williams R
J Pathol. 1979 Jul;128(3):159-62. doi: 10.1002/path.1711280307.
A 50-year-old man presented with abdominal pain followed by marked liver and renal dysfunction. Although liver scan appearances were not diagnostic, at laparotomy a tense, enlarged liver was found with thrombosis of the inferior vena cava. Despite full supportive measures the patient died within a month of laparotomy. Subsequent necropsy confirmed the diagnosis of Budd Chiari syndrome and revealed the primary cause to be a myosarcoma of the right atrium, an occurrence hitherto unreported.
一名50岁男性患者,先是出现腹痛,随后出现明显的肝肾功能障碍。尽管肝脏扫描结果不具有诊断性,但剖腹探查时发现肝脏紧张、肿大,下腔静脉有血栓形成。尽管采取了全面的支持措施,患者仍在剖腹探查后一个月内死亡。随后的尸检证实了布加综合征的诊断,并揭示其主要病因是右心房平滑肌肉瘤,这种情况迄今尚未见报道。