Vale Lia Rachel Gomes do, Coeli Flávia Regina, Michalany Nilceo, Hassun Karime Marques, Porro Adriana Maria
Universidade Federal de São Paulo - São Paulo (SP), Brasil.
An Bras Dermatol. 2009 Mar-Apr;84(2):190-3. doi: 10.1590/s0365-05962009000200014.
Pachydermodactyly is a rare form of digital fibromatosis involving the proximal portions of the fingers that usually affects young males. We present a 25-year-old male patient with a two year history of asymptomatic nodules in the fingers. Three months before the visit, he had observed similar lesions on the feet and right knee. Histopathological analysis showed thickened dermis with proliferation of fibroblasts and collagenous fibers, with deposition of mucinous material. This represents a rare case of pachydermodactyly of transgrediens form.
厚皮性厚骨膜病是一种罕见的数字纤维瘤病，累及手指近端，通常影响年轻男性。我们报告一例25岁男性患者，手指出现无症状结节已有两年病史。就诊前三个月，他在足部和右膝发现了类似病变。组织病理学分析显示真皮增厚，有成纤维细胞和胶原纤维增生，伴有黏液样物质沉积。这是一例罕见的侵袭性厚皮性厚骨膜病。
