Department of Neurology, Aeghinition Hospital, University of Athens, 74, Vassilissis Sofias Avenue, 11528 Athens, Greece.
Neurol Sci. 2009 Dec;30(6):495-7. doi: 10.1007/s10072-009-0140-9. Epub 2009 Sep 19.
Alpha 62-year-old man was presented with bilateral cataract, proximal muscle weakness and difficulty in relaxing the hands after voluntary contraction. Idiopathic hypoparathyroidism was diagnosed. Electrophysiological study showed spontaneous motor unit action potentials, occurring and disappearing abruptly, as duplets, triplets and multiplets, with an intra-burst frequency of up to 100 Hz and some of them waning in amplitude, findings consistent with neuromyotonia.
一位 62 岁的男性患者,表现为双侧白内障,近端肌肉无力,自愿收缩后手难以放松。诊断为特发性甲状旁腺功能减退症。电生理研究显示自发运动单位动作电位,呈双相、三相和多相,突发突止,爆发频率高达 100Hz,部分波幅递减,这些表现符合肌纤维颤搐。