McDougal W S, MacDonell R C
Department of Urology, Vanderbilt University School of Medicine, Nashville, Tennessee 37232-2765.
J Urol. 1991 Jan;145(1):112-4. doi: 10.1016/s0022-5347(17)38263-0.
Idiopathic retroperitoneal fibrosis is exceedingly uncommon in childhood and its etiology is uncertain. Support for an immunological basis for the disease is given by a report of a 14-year-old girl with severe retroperitoneal fibrosis causing progressive azotemia in whom azathioprine and prednisolone were used successfully. This case supports the efficacy of immunotherapy in the treatment of idiopathic retroperitoneal fibrosis.
特发性腹膜后纤维化在儿童期极为罕见，其病因尚不确定。一名14岁女孩患有严重的腹膜后纤维化并导致进行性氮质血症，使用硫唑嘌呤和泼尼松龙治疗成功，这一病例报告为该疾病的免疫基础提供了支持。该病例支持免疫疗法在治疗特发性腹膜后纤维化中的疗效。
