Department of Anesthesiology, Perioperative Medicine and Pain Treatment, Shaare Zedek Medical Center, Hebrew University, Jerusalem, Israel.
Int J Obstet Anesth. 2010 Jan;19(1):106-8. doi: 10.1016/j.ijoa.2009.07.002. Epub 2009 Nov 28.
Patients with cleidocranial dysplasia, a rare autosomal dominant genetic syndrome, possess abnormal anatomical features of the head, mouth, neck and spinal column. These features may result in perioperative problems such as difficult airway and complicated regional anesthesia. We report the anesthetic management of a young woman with cleidocranial dysplasia undergoing four caesarean sections, one vaginal delivery and a dilatation and curettage, employing different modes of anesthesia. Anesthetic management in this disorder presents challenges for both general and neuraxial anesthesia.
患有颅锁骨发育不全症(一种罕见的常染色体显性遗传综合征)的患者,其头部、口腔、颈部和脊柱具有异常的解剖结构。这些特征可能导致围手术期问题,例如气道困难和复杂的区域麻醉。我们报告了一位年轻女性患有颅锁骨发育不全症,她经历了四次剖宫产、一次阴道分娩和一次扩张刮宫术,采用了不同的麻醉方式。这种疾病的麻醉管理对全身麻醉和神经轴麻醉都提出了挑战。