• 文献检索
  • 文档翻译
  • 深度研究
  • 学术资讯
  • Suppr Zotero 插件Zotero 插件
  • 邀请有礼
  • 套餐&价格
  • 历史记录
应用&插件
Suppr Zotero 插件Zotero 插件浏览器插件Mac 客户端Windows 客户端微信小程序
定价
高级版会员购买积分包购买API积分包
服务
文献检索文档翻译深度研究API 文档MCP 服务
关于我们
关于 Suppr公司介绍联系我们用户协议隐私条款
关注我们

Suppr 超能文献

核心技术专利：CN118964589B侵权必究
粤ICP备2023148730 号-1Suppr @ 2026

文献检索

告别复杂PubMed语法，用中文像聊天一样搜索，搜遍4000万医学文献。AI智能推荐，让科研检索更轻松。

立即免费搜索

文件翻译

保留排版，准确专业，支持PDF/Word/PPT等文件格式，支持 12+语言互译。

免费翻译文档

深度研究

AI帮你快速写综述，25分钟生成高质量综述，智能提取关键信息，辅助科研写作。

立即免费体验

SLE with C1q deficiency treated with fresh frozen plasma: a 10-year experience.

作者信息

Mehta Puja, Norsworthy Peter J, Hall Angela E, Kelly Susan J, Walport Mark J, Botto Marina, Pickering Matthew C

出版信息

Rheumatology (Oxford). 2010 Apr;49(4):823-4. doi: 10.1093/rheumatology/kep387. Epub 2009 Dec 4.

DOI:10.1093/rheumatology/kep387
PMID:19965977
Abstract
摘要

相似文献

1
SLE with C1q deficiency treated with fresh frozen plasma: a 10-year experience.用新鲜冷冻血浆治疗C1q缺乏的系统性红斑狼疮：十年经验
Rheumatology (Oxford). 2010 Apr;49(4):823-4. doi: 10.1093/rheumatology/kep387. Epub 2009 Dec 4.
2
Hereditary C1q deficiency and systemic lupus erythematosus.遗传性C1q缺乏与系统性红斑狼疮
QJM. 1994 Aug;87(8):455-64.
3
Systemic lupus erythematosus with C1q deficiency: treatment with fresh frozen plasma.伴有C1q缺乏的系统性红斑狼疮：新鲜冷冻血浆治疗
Lupus. 2018 Jan;27(1):134-138. doi: 10.1177/0961203317741565. Epub 2017 Nov 7.
4
Combination of ofatumumab and fresh frozen plasma in hypocomplementemic systemic lupus erythematosus: a case report.奥法木单抗与新鲜冷冻血浆联合治疗低补体血症性系统性红斑狼疮：一例报告
Lupus. 2018 Jul;27(8):1395-1396. doi: 10.1177/0961203318756289. Epub 2018 Feb 13.
5
Rapid improvement of SLE-specific cutaneous lesions by C1q immunoadsorption.通过C1q免疫吸附快速改善系统性红斑狼疮特异性皮肤病变
Ann Rheum Dis. 2001 Sep;60(9):898-9.
6
Complement C1q and C8beta deficiency in an individual with recurrent bacterial meningitis and adult-onset systemic lupus erythematosus-like illness.一名复发性细菌性脑膜炎和成人期系统性红斑狼疮样疾病患者存在补体C1q和C8β缺乏。
Rheumatology (Oxford). 2008 Oct;47(10):1588-9. doi: 10.1093/rheumatology/ken289. Epub 2008 Aug 4.
7
Marked variability in clinical presentation and outcome of patients with C1q immunodeficiency.C1q 免疫缺陷患者的临床表现和预后存在显著差异。
J Autoimmun. 2015 Aug;62:39-44. doi: 10.1016/j.jaut.2015.06.002. Epub 2015 Jun 26.
8
Analysis of C1q polymorphisms suggests association with systemic lupus erythematosus, serum C1q and CH50 levels and disease severity.C1q多态性分析表明其与系统性红斑狼疮、血清C1q及总补体活性水平以及疾病严重程度相关。
Ann Rheum Dis. 2009 May;68(5):715-20. doi: 10.1136/ard.2007.085688. Epub 2008 May 26.
9
Anti-chromatin and anti-C1q antibodies in systemic lupus erythematosus compared to other systemic autoimmune diseases.系统性红斑狼疮中抗染色质抗体和抗C1q抗体与其他系统性自身免疫性疾病的比较。
Scand J Rheumatol. 2007 Jul-Aug;36(4):291-8. doi: 10.1080/03009740701218717.
10
C1q inhibits immune complex-induced interferon-alpha production in plasmacytoid dendritic cells: a novel link between C1q deficiency and systemic lupus erythematosus pathogenesis.C1q抑制浆细胞样树突状细胞中免疫复合物诱导的α干扰素产生：C1q缺陷与系统性红斑狼疮发病机制之间的新联系。
Arthritis Rheum. 2009 Oct;60(10):3081-90. doi: 10.1002/art.24852.

引用本文的文献

1
Mechanism and target treatment of primary immunodeficiency diseases with systemic lupus erythematosus-like phenotype.具有系统性红斑狼疮样表型的原发性免疫缺陷病的机制与靶向治疗
Pediatr Discov. 2024 May 27;2(3):e67. doi: 10.1002/pdi3.67. eCollection 2024 Sep.
2
Drug-resistant epilepsy associated with peripheral complement decreases and sex-specific cytokine imbalances: a pilot study.与外周补体减少和性别特异性细胞因子失衡相关的耐药性癫痫：一项初步研究。
Sci Rep. 2025 Feb 11;15(1):5096. doi: 10.1038/s41598-025-88654-5.
3
Two siblings with monogenic lupus due to C1qC deficiency and case based review.
两名因C1qC缺乏导致单基因狼疮的兄弟姐妹及病例回顾
Clin Rheumatol. 2025 Mar;44(3):1355-1365. doi: 10.1007/s10067-025-07333-y. Epub 2025 Jan 22.
4
Hematopoietic Stem Cell Transplantation for C1q Deficiency: A Study on Behalf of the EBMT Inborn Errors Working Party.C1q缺陷的造血干细胞移植：代表欧洲血液与骨髓移植学会先天性疾病工作组开展的一项研究
J Clin Immunol. 2024 Oct 29;45(1):35. doi: 10.1007/s10875-024-01819-1.
5
Sex-Specific Complement and Cytokine Imbalances in Drug-Resistant Epilepsy: Biomarkers of Immune Vulnerability.耐药性癫痫中性别特异性补体和细胞因子失衡：免疫易损性的生物标志物
bioRxiv. 2024 Sep 18:2024.09.16.612934. doi: 10.1101/2024.09.16.612934.
6
Hereditary C1q Deficiency is Associated with Type 1 Interferon-Pathway Activation and a High Risk of Central Nervous System Inflammation.遗传性 C1q 缺陷与 1 型干扰素通路激活和中枢神经系统炎症高风险相关。
J Clin Immunol. 2024 Aug 28;44(8):185. doi: 10.1007/s10875-024-01788-5.
7
Complements and Their Role in Systemic Disorders.补体及其在全身性疾病中的作用。
Cureus. 2024 Jan 26;16(1):e52991. doi: 10.7759/cureus.52991. eCollection 2024 Jan.
8
Vasculitis and vasculopathy associated with inborn errors of immunity: an overview.与遗传性免疫缺陷相关的血管炎和血管病变：概述
Front Pediatr. 2024 Jan 31;11:1258301. doi: 10.3389/fped.2023.1258301. eCollection 2023.
9
The complement system and human autoimmune diseases.补体系统与人类自身免疫性疾病。
J Autoimmun. 2023 May;137:102979. doi: 10.1016/j.jaut.2022.102979. Epub 2022 Dec 18.
10
Predicting diagnostic gene expression profiles associated with immune infiltration in patients with lupus nephritis.预测狼疮肾炎患者免疫浸润相关的诊断基因表达谱。
Front Immunol. 2022 Dec 2;13:839197. doi: 10.3389/fimmu.2022.839197. eCollection 2022.