Stürmer K, Hunzelmann N, Beutner D
Klinik und Poliklinik für Hals-Nasen-Ohrenheilkunde, Universität zu Köln, Joseph-Stelzmann-Str. 9, 50924, Köln, Deutschland.
HNO. 2010 Apr;58(4):374-7. doi: 10.1007/s00106-009-2016-y.
Scleredema adultorum Buschke is a rare disease of unknown etiology characterized by an immovable edematous swelling and hardening of the skin which typically begins in the neck and spreads to the face, head, shoulders and thorax. No standardized therapy for scleredema adultorum Buschke has yet been established. As in the case of our patient, a systemic cortisone therapy is normally administered combined with high-dose penicillin and physiotherapy.
布施克成人硬肿病是一种病因不明的罕见疾病,其特征为皮肤出现固定性水肿性肿胀和硬化,通常始于颈部,然后蔓延至面部、头部、肩部和胸部。目前尚未确立针对布施克成人硬肿病的标准化治疗方法。就我们的患者而言,通常会采用全身皮质激素疗法,同时结合大剂量青霉素和物理治疗。