Sudhalter V, Scarborough H S, Cohen I L
New York State Office of Mental Retardation and Developmental Disabilities, New York State Institute for Basic Research Developmental Disabilities, Staten Island 10314.
Am J Med Genet. 1991 Feb-Mar;38(2-3):493-7. doi: 10.1002/ajmg.1320380270.
The expressive language of 19 fragile X [fra(X)] males with chronological ages between 5 and 36 years and Vineland Adaptive Behavior Scores between 21 and 79 was examined for syntactic as well as pragmatic proficiency. The production of deviant repetitive language was observed with this group, corroborating the results of an earlier study with a smaller sample of fra(X) males. In contrast, when 2 syntax scores, mean length of utterance (MLU), and Index of Productive Syntax (IPSyn) were derived from naturalistic language observations, the relation of complexity to length was observed to be very similar to the known relationship of these 2 facets of syntactic ability in normal preschoolers. These results, and the absence of correlations between syntactic scores and proportions of deviant repetitive language are consistent with the notion that the syntactic development of fra(X) males is typically delayed rather than deviant. For effective assessment and remediation of communicative problems associated with the syndrome to be developed, it is argued, language must be considered as a combination of competencies rather than as a unitary skill.
对19名年龄在5至36岁之间、文兰适应性行为得分在21至79之间的脆性X综合征[fra(X)]男性的表达性语言进行了句法和语用能力方面的检查。在这组人群中观察到了异常重复语言的产生，这证实了早期一项针对较小样本的fra(X)男性研究的结果。相比之下，当从自然语言观察中得出两个句法得分、平均语句长度（MLU）和句法生成指数（IPSyn）时，观察到复杂性与长度之间的关系与正常学龄前儿童句法能力这两个方面的已知关系非常相似。这些结果，以及句法得分与异常重复语言比例之间不存在相关性，都与fra(X)男性的句法发展通常是延迟而非异常的观点一致。有人认为，为了开发与该综合征相关的沟通问题的有效评估和补救方法，必须将语言视为多种能力的组合，而不是单一技能。
