Bentur L, Canny G, Thorner P, Superina R, Babyn P, Levison H
Division of Chest Medicine, Hospital for Sick Children, Toronto, Canada.
Chest. 1991 May;99(5):1292-3. doi: 10.1378/chest.99.5.1292.
Pneumothorax is a rare presentation of congenital cystic adenomatoid malformation (CCAM) in the newborn period and is presumed to be due to resuscitative measures. A previously well three-week-old baby presented with spontaneous tension pneumothorax due to CCAM. In the lung resection specimen, a malformation was seen, which in addition to the histologic changes of CCAM, showed diffuse vascular proliferation in the interstitium and lining of air space by type 2 pneumocytes. We propose that this is a new variant of CCAM rather than one of the classic three types. The unusual clinical manifestation may be related to the unusual histologic features.
气胸是新生儿先天性囊性腺瘤样畸形（CCAM）的一种罕见表现，推测与复苏措施有关。一名此前健康的三周大婴儿因CCAM出现自发性张力性气胸。在肺切除标本中，可见一种畸形，除了CCAM的组织学改变外，间质和肺泡内衬可见2型肺泡上皮细胞弥漫性血管增生。我们认为这是CCAM的一种新变体，而非经典三种类型之一。这种不寻常的临床表现可能与不寻常的组织学特征有关。
