Rosenstiel Basic Medical Sciences Research Center and Department of Biology, Brandeis University, Waltham, MA, USA.
Blood. 2010 Apr 29;115(17):3598-605. doi: 10.1182/blood-2009-03-213876. Epub 2010 Mar 3.
Activating mutations of NRAS are common in acute myeloid leukemia, chronic myelomonocytic leukemia, and myelodysplastic syndrome. Like all RAS proteins, NRAS must undergo a series of post-translational modifications for differential targeting to distinct membrane subdomains. Although farnesylation is the obligatory first step in post-translational modifications of RAS, to date, successes of therapies targeting farnesyl protein transferase are modest. Other RAS modifications, such as palmitoylation, are required for optimal plasma membrane association of RAS proteins. However, the relative importance of these latter modifications of RAS in leukemogenesis is not clear. We have previously shown that expression of oncogenic NRAS using a bone marrow transduction and transplantation model efficiently induces a chronic myelomonocytic leukemia- or acute myeloid leukemia-like disease in mice. Here we examined the role of palmitoylation in NRAS leukemogenesis using this model. We found that palmitoylation is essential for leukemogenesis by oncogenic NRAS. We also found that farnesylation is essential for NRAS leukemogenesis, yet through a different mechanism from that of palmitoylation deficiency. This study demonstrates, for the first time, that palmitoylation is an essential process for NRAS leukemogenesis and suggests that the development of therapies targeting RAS palmitoylation may be effective in treating oncogenic NRAS-associated malignancies.
NRAS 的激活突变常见于急性髓性白血病、慢性髓单核细胞白血病和骨髓增生异常综合征。与所有 RAS 蛋白一样,NRAS 必须经历一系列翻译后修饰,以靶向不同的膜亚区。虽然法呢基化是 RAS 翻译后修饰的必需第一步,但迄今为止,针对法尼基蛋白转移酶的治疗方法的成功是有限的。其他 RAS 修饰,如棕榈酰化,对于 RAS 蛋白与质膜的最佳结合是必需的。然而,这些 RAS 修饰在后在白血病发生中的相对重要性尚不清楚。我们之前曾使用骨髓转导和移植模型展示了表达致癌性 NRAS 可有效地在小鼠中诱导慢性髓单核细胞白血病样或急性髓性白血病样疾病。在这里,我们使用该模型研究了棕榈酰化在 NRAS 白血病发生中的作用。我们发现棕榈酰化对于致癌性 NRAS 的白血病发生是必需的。我们还发现法尼基化对于 NRAS 白血病发生是必需的,但与棕榈酰化缺陷的机制不同。这项研究首次证明了棕榈酰化是 NRAS 白血病发生的一个必需过程,并表明针对 RAS 棕榈酰化的治疗方法的开发可能对治疗致癌性 NRAS 相关恶性肿瘤有效。