Department of Medical imaging, Kaohsiung Medical University Hospital, Kaohsiung, Taiwan.
Kaohsiung J Med Sci. 2010 Mar;26(3):154-7. doi: 10.1016/S1607-551X(10)70023-1.
Kaposiform hemangioendothelioma is a very infrequent, locally aggressive vascular neoplasm, characterized by fascicular spindle cell proliferation. It occurs almost exclusively in infants and adolescents, and is often associated with Kasabach-Merritt phenomenon. The tumor is predominantly located subcutaneously or in the deep soft tissue of the extremities and trunk, peritoneum, or retroperitoneum. However, this tumor can sometimes be located on the head and neck. We report a case of kaposiform hemangioendothelioma of the maxillary sinus in a 4-month-old female infant presenting with cheek swelling, thrombocytopenia, anemia, and disseminated intravascular coagulation. Sinus computed tomography presented an enhancing, bone-destructing tumor. Magnetic resonance images showed an uncommon appearance as mostly low signal intensity on T2-weighted images.
卡波西样血管内皮细胞瘤是一种非常罕见的局部侵袭性血管肿瘤，其特征是束状梭形细胞增生。它几乎只发生在婴儿和青少年中，常伴有卡-梅现象。肿瘤主要位于皮下或四肢和躯干的深部软组织、腹膜或后腹膜。然而，这种肿瘤有时也可位于头颈部。我们报告了一例 4 个月大女性婴儿上颌窦卡波西样血管内皮细胞瘤病例，表现为脸颊肿胀、血小板减少、贫血和弥散性血管内凝血。鼻窦计算机断层扫描显示一个增强的、破坏骨的肿瘤。磁共振成像显示出一种不常见的表现，即 T2 加权图像上主要为低信号强度。
