Kim Ji Bak, Kim Seong Hwan, Lim Sang Yup, Roh Seung Young, Cho Goo-Yeong, Song Hye Jong, Park Silvia, Lee Jeeyun, Kim Seok Jin
Department of Medicine, Korea University Ansan Hospital, Ansan, South Korea.
Echocardiography. 2010 Feb;27(2):E23-6. doi: 10.1111/j.1540-8175.2009.01059.x.
We present a case of primary angiosarcoma of the pulmonary trunk that was initially misdiagnosed as a subacute massive pulmonary thromboembolism in a 26-year-old woman. This is an extremely rare disease that is usually indistinguishable from acute or chronic thromboembolic disease of the pulmonary arteries because the clinical and radiologic findings of pulmonary artery angiosarcoma are similar to those of pulmonary thromboembolism. Although the incidence of pulmonary artery angiosarcoma is very low, our case demonstrates that this disease entity should be included in the differential diagnosis of pulmonary thromboembolism, especially in patients who do not respond to anticoagulant therapy or present with no identifiable source of thromboembolic events.
我们报告一例26岁女性原发性肺动脉干血管肉瘤病例，该病例最初被误诊为亚急性大面积肺血栓栓塞症。这是一种极其罕见的疾病，通常无法与肺动脉急性或慢性血栓栓塞性疾病区分开来，因为肺动脉血管肉瘤的临床和影像学表现与肺血栓栓塞症相似。尽管肺动脉血管肉瘤的发病率很低，但我们的病例表明，在肺血栓栓塞症的鉴别诊断中应考虑到这种疾病实体，尤其是在对抗凝治疗无反应或无明确血栓栓塞事件来源的患者中。
