Mahajan Abhishek, Rekhi Bharat, Laskar Siddhartha, Bajpai Jyoti, Jayasree Lekshmy, Thakur Meenakshi H
Department of Radiodiagnosis and Imaging, Tata Memorial Hospital, Tata Memorial Centre, Room No 120, Dr E Borges Road, Parel, Mumbai, Maharashtra 400012 India.
Department of Pathology, Tata Memorial Hospital, Tata Memorial Centre, Mumbai, Maharashtra 400012 India.
Clin Sarcoma Res. 2017 Jul 1;7:13. doi: 10.1186/s13569-017-0080-8. eCollection 2017.
Primary pulmonary artery sarcomas are rare malignant vascular tumors and carry a very poor prognosis. Due to overlapping clinical and radiological features, the differentiation between pulmonary artery thromboembolism and pulmonary artery sarcoma can be challenging.
We herein present clinical, radiological and pathological features of primary pulmonary artery high grade sarcoma (angiosarcoma) in a 59-year-old male. The patient presented with a history of breathlessness on exertion of 2-months duration and was misdiagnosed as massive pulmonary thromboembolism on initial CT imaging.
Great similarity with significant degree of overlap in clinical and radiologic presentation makes differentiation of pulmonary artery sarcomas and thromboembolism a diagnostic challenge. Even though they are exceptionally rare, one should always consider it as differential diagnosis especially in cases with atypical clinical or imaging presentation.
原发性肺动脉肉瘤是罕见的恶性血管肿瘤，预后极差。由于临床和放射学特征重叠，肺动脉血栓栓塞与肺动脉肉瘤的鉴别诊断具有挑战性。
我们在此呈现一名59岁男性原发性肺动脉高级别肉瘤（血管肉瘤）的临床、放射学和病理学特征。患者有2个月的劳力性呼吸困难病史，初始CT成像时被误诊为大面积肺血栓栓塞。
临床和放射学表现高度相似且重叠程度大，使得肺动脉肉瘤与血栓栓塞的鉴别成为一项诊断挑战。尽管它们极为罕见，但尤其在临床或影像学表现不典型的病例中，应始终将其视为鉴别诊断。
