Bhagwat Krishna, Hallam Jane, Antippa Phillip, Larobina Marco
Department of Cardiothoracic Surgery, Royal Melbourne Hospital, Parkville, Australia.
Interact Cardiovasc Thorac Surg. 2012 Mar;14(3):342-4. doi: 10.1093/icvts/ivr087. Epub 2011 Dec 6.
Primary angiosarcoma of pulmonary artery is a very rare lesion. We present a case of primary angiosarcoma that was initially misdiagnosed as a subacute massive pulmonary thromboembolism in a 30-year-old man. This rare disease is usually indistinguishable from acute or chronic thromboembolic disease of the pulmonary arteries. The clinical and radiological findings of pulmonary artery angiosarcoma are similar to those of pulmonary thromboembolism. Although the incidence of pulmonary artery angiosarcoma is very low, our case demonstrates that this disease entity should be included in the differential diagnosis of pulmonary thromboembolism. Patients with early identification can have curative potential with aggressive surgical intervention.
肺动脉原发性血管肉瘤是一种非常罕见的病变。我们报告一例原发性血管肉瘤病例，该病例最初在一名30岁男性中被误诊为亚急性大面积肺血栓栓塞症。这种罕见疾病通常与肺动脉急性或慢性血栓栓塞性疾病难以区分。肺动脉血管肉瘤的临床和影像学表现与肺血栓栓塞症相似。尽管肺动脉血管肉瘤的发病率非常低，但我们的病例表明，在肺血栓栓塞症的鉴别诊断中应考虑到这种疾病实体。早期确诊的患者通过积极的手术干预可能具有治愈潜力。
