Continuous venovenous hemofiltration in the management of acute decompensation in inborn errors of metabolism.
作者信息
Thompson G N, Butt W W, Shann F A, Kirby D M, Henning R D, Howells D W, Osborne A
机构信息
Department of Paediatrics, University of Melbourne, Murcoch Institute, Australia.
出版信息
J Pediatr. 1991 Jun;118(6):879-84. doi: 10.1016/s0022-3476(05)82198-5.
PMID:2040923
Abstract
Continuous venovenous hemofiltration was used to treat two neonates, one with maple syrup urine disease and the other with an inborn error of long-chain fatty acid oxidation. The latter infant had hypoglycemia, hyperammonemia and lactic acidosis. In both cases, acceptable biochemical control was achieved within 8 hours. This therapy offers the potential to overcome acute crises rapidly in a wide range of inborn errors of intermediary metabolism.
摘要
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