Department of Radiology, Loyola University Health System, Maywood, IL 60153, USA.
Pediatr Radiol. 2010 Sep;40(9):1562-5. doi: 10.1007/s00247-010-1670-2. Epub 2010 May 4.
Pulmonary interstitial glycogenosis (PIG) is a rare pediatric interstitial lung disease. We report a case of a term boy presenting with tachypnea at birth requiring supplemental oxygen. Chest radiographs followed by high-resolution CT (HRCT) demonstrated hyperinflation and diffuse interstitial markings interspersed with multiple cystic spaces. An open lung biopsy demonstrated a minor component of PIG superimposed upon poor alveolarization. PIG in the setting of lung growth abnormality might be more common than previously described. Additionally, radiographic findings associated with most pediatric interstitial lung diseases are nonspecific, and histopathologic correlation is essential for diagnosis.
肺间质糖原沉积症（PIG）是一种罕见的儿科间质性肺病。我们报告了一例足月男婴出生时即出现呼吸急促，需要补充氧气。胸部 X 线片和高分辨率 CT（HRCT）显示过度充气和弥漫性间质条纹，伴有多个囊状空间。开胸肺活检显示 PIG 伴有肺泡化不良。肺生长异常伴 PIG 可能比以前描述的更为常见。此外，大多数儿科间质性肺疾病的影像学表现无特异性，组织病理学相关性对诊断至关重要。
