Couffinhal T, Bonnet J, Benchimol D, Dos Santos P, Besse P, Bricaud H
Hôpital Cardiologique, Pessac, France.
Eur Heart J. 1991 Feb;12(2):266-9. doi: 10.1093/oxfordjournals.eurheartj.a059878.
We report a case of Budd Chiari syndrome associated with a deficit in protein C, in a young women admitted to hospital for investigation of thromboembolic disease and ascites. This coagulation defect was thought to be an aetiological factor in the suprahepatic vein thrombosis. The diagnosis and treatment of this rare form of the syndrome are discussed.
我们报告一例布加综合征合并蛋白C缺乏症的病例，患者为一名年轻女性，因血栓栓塞性疾病和腹水入院接受检查。这种凝血缺陷被认为是肝上静脉血栓形成的一个病因。本文讨论了这种罕见综合征的诊断和治疗。
