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一例皮肤血管平滑肌脂肪瘤。

A case of a cutaneous angiomyolipoma.

作者信息

Shin Jung-U, Lee Kyu-Yeoop, Roh Mi Ryung

机构信息

Department of Dermatology and Cutaneous Biology Research Institute, Yonsei University College of Medicine, Seoul, Korea.

出版信息

Ann Dermatol. 2009 May;21(2):217-20. doi: 10.5021/ad.2009.21.2.217. Epub 2009 May 31.

Abstract

A cutaneous angiomyolipoma, which is also known as a cutaneous angiolipoleiomyoma, is a rare benign mesenchymal tumor. Only 18 cases have been reported in the English literature. We describe a case of an angiomyolipoma presenting on the right ear helix of a 26-year-old female. The histopathologic examination revealed a typical form of an angiomyolipoma with a proliferation of mature adipocytes. As with all previously reported cases, our patient did not present with the stigmata of tuberous sclerosis. This is the 20th reported case of cutaneous angiomyolipoma and the 3rd reported case in Korea.

摘要

皮肤血管平滑肌脂肪瘤,也被称为皮肤血管脂肪平滑肌瘤,是一种罕见的良性间叶组织肿瘤。英文文献中仅报道过18例。我们描述了一例发生在一名26岁女性右耳螺旋上的血管平滑肌脂肪瘤病例。组织病理学检查显示为血管平滑肌脂肪瘤的典型形态,伴有成熟脂肪细胞的增生。与之前所有报道的病例一样,我们的患者没有结节性硬化症的体征。这是第20例报道的皮肤血管平滑肌脂肪瘤病例,也是韩国报道的第3例。

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