Sirinoglu Hakan, Sönmez Ahmet, Sav Aydin, Numanoglu Ayhan
Department of Plastic, Reconstructive and Aesthetic Surgery, Marmara University Medical School, Istanbul, Turkey.
Ann Plast Surg. 2010 Aug;65(2):174-6. doi: 10.1097/SAP.0b013e3181c9c41b.
Lipofibromatous hamartoma is a rare tumor-like overgrowth of fibroadipose tissue surrounding the nerves. Most commonly, it involves the median nerve. The tumor is usually present at birth and grows very slowly. The expected age of clinical presentation is the third or fourth decades of life. The case reported here had a rapid overgrowth and presented at the age of eight. Our case is the first reported case of lipofibromatous hamartoma of the median nerve in the pediatric age group.
脂肪纤维瘤性错构瘤是一种罕见的肿瘤样病变，表现为神经周围纤维脂肪组织过度生长。最常见的是累及正中神经。该肿瘤通常在出生时就存在，生长非常缓慢。临床表现的预期年龄为生命的第三个或第四个十年。此处报告的病例生长迅速，8岁时出现症状。我们的病例是小儿年龄组中首例报告的正中神经脂肪纤维瘤性错构瘤。
