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保守治疗 Herlyn-Werner-Wunderlich 苗勒管混合体畸形变异型、无沟通单侧中肾管残迹合并 Gartner 管假囊肿

Conservative treatment of a Herlyn-Werner-Wunderlich müllerian anomaly variant, noncommunicating hemiuterus with Gartner duct pseudocyst.

机构信息

Department of Obstetrics and Gynecology, University of Utah Health Sciences Center, Salt Lake City, UT 84132, USA.

出版信息

J Minim Invasive Gynecol. 2011 Mar-Apr;18(2):262-6. doi: 10.1016/j.jmig.2010.12.006.

DOI:10.1016/j.jmig.2010.12.006
PMID:21354076
Abstract

Asymmetric obstructed uterus didelphys (Herlyn-Werner-Wunderlich syndrome) is a rare congenital müllerian anomaly consisting of uterus didelphys, hemivaginal septum, and ipsilateral renal agenesis. Herein is reported a case of incomplete Herlyn-Werner-Wunderlich syndrome diagnosed using 3-dimensional transvaginal ultrasound in a 14-year-old patient with absence of the hemivaginal septum. The most contributive diagnostic factors and appropriate therapeutic management in such cases are discussed.

摘要

不对称性双子宫(赫尔林-韦纳-武德希综合征)是一种罕见的先天性苗勒管畸形,由双子宫、半隔阴道和同侧肾发育不全组成。本文报告了一例 14 岁患者经三维经阴道超声诊断为不完全性赫尔林-韦纳-武德希综合征,该患者无半隔阴道。讨论了此类病例最有帮助的诊断因素和适当的治疗管理。

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Conservative treatment of a Herlyn-Werner-Wunderlich müllerian anomaly variant, noncommunicating hemiuterus with Gartner duct pseudocyst.保守治疗 Herlyn-Werner-Wunderlich 苗勒管混合体畸形变异型、无沟通单侧中肾管残迹合并 Gartner 管假囊肿
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[Asymmetric obstructed uterus didelphys/incomplete Herlyn-Werner-Wunderlich syndrome/diagnosed by transvaginal 3D ultrasound--a case report].
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Hemivaginal septum resection in a patient with a rare variant of Herlyn-Werner-Wunderlich syndrome.对一名患有罕见变异型赫林-韦纳-温德利希综合征患者进行半阴道隔切除术。
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Herlyn-Werner-Wunderlich syndrome consisting of uterine didelphys, obstructed hemivagina and ipsilateral renal agenesis in a newborn.新生儿子宫双角、阴道闭锁并同侧肾发育不全的 Herlyn-Werner-Wunderlich 综合征。
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引用本文的文献

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Herlyn-Werner-Wunderlich syndromne: case review and report of the literature.赫勒林-韦纳-武德希利综合征:病例回顾及文献报告。
Rev Colomb Obstet Ginecol. 2021 Dec 30;72(4):407-422. doi: 10.18597/rcog.3699.
2
Herlyn-Werner-Wunderlich syndrome: An "early" onset case report and review of Literature.赫林-韦纳-温德利希综合征:一例“早发性”病例报告及文献综述。
Int J Surg Case Rep. 2015;11:59-63. doi: 10.1016/j.ijscr.2015.04.027. Epub 2015 Apr 24.