Department of Pediatrics, Chung Shan Medical University Hospital, Taichung, Taiwan.
Pediatr Neonatol. 2012 Feb;53(1):68-71. doi: 10.1016/j.pedneo.2011.11.014. Epub 2012 Jan 24.
Herlyn-Werner-Wunderlich (HWW) syndrome is a rare variant of Müllerian duct anomalies consisting of uterine didelphys, obstructed hemivagina, and ipsilateral renal agenesis. Patients with HWW syndrome are usually asymptomatic until menarche, when they present with acute lower abdominal pain. Here we report a case of a female newborn with right renal agenesis diagnosed during the pregnancy. The patient presented with a protruding mass over the vaginal introitus that was associated with an obstructed hemivagina and uterine didelphys.
赫尔林-韦纳-旺德雷希（HWW）综合征是一种罕见的苗勒管畸形变异，其特征为双子宫、阴道半横隔和同侧肾发育不全。HWW 综合征患者通常无症状，直到月经初潮时才会出现急性下腹痛。本研究报告了一例在妊娠期间诊断为右侧肾发育不全的女性新生儿病例。患者的阴道入口处有一个突出的肿块，伴有阴道半横隔和双子宫。
