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一名患有与渗出性缩窄性心包炎相关的右心衰竭的女孩。

A girl with right heart failure related to effusive-constrictive pericarditis.

作者信息

Chen Meng-Yu, Chen Yih-Sharng, Chen Shyh-Jye, Lu Chun-Wei

机构信息

Department of Pediatrics, National Taiwan University Hospital, No 8, Chung-San South Road, Taipei 100, Taiwan.

出版信息

Pediatr Cardiol. 2011 Jun;32(5):681-4. doi: 10.1007/s00246-011-9927-6. Epub 2011 Feb 27.

DOI:10.1007/s00246-011-9927-6
PMID:21359949
Abstract

Effusive-constrictive pericarditis is characterized by constriction of visceral pericardium with a coexisting tense pericardial effusion. We report a 10-year-old girl with right heart failure due to effusive-constrictive pericarditis. She did not present typical features, such as cardiac tamponade or thickening of pericardium (visceral and parietal), but constrictive physiology was observed by echocardiography and cardiac computed tomography. These noninvasive imaging modalities provided clinical clues to make precise diagnosis. The patient underwent surgical drainage of pericardial fluid and visceral pericardiectomy, which resulted in improved hemodynamics and symptoms.

摘要

渗出-缩窄性心包炎的特征是脏层心包缩窄并伴有同时存在的大量心包积液。我们报告了一名10岁因渗出-缩窄性心包炎导致右心衰竭的女孩。她未表现出典型特征,如心脏压塞或心包(脏层和壁层)增厚,但超声心动图和心脏计算机断层扫描观察到缩窄性生理改变。这些非侵入性成像方式为做出准确诊断提供了临床线索。患者接受了心包积液手术引流和脏层心包切除术,血流动力学和症状均得到改善。

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A 63-year-old woman with a pericardial effusion, bilateral pleural effusions, and ascites: is the whole greater than the sum of its parts?一名患有心包积液、双侧胸腔积液和腹水的63岁女性:整体是否大于部分之和?
Echocardiography. 2010 Apr;27(4):454-9. doi: 10.1111/j.1540-8175.2009.01110.x.
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Effusive constrictive pericarditis: 2D, 3D echocardiography and MRI imaging.渗出性缩窄性心包炎:二维、三维超声心动图及磁共振成像
Echocardiography. 2007 Nov;24(10):1110-4. doi: 10.1111/j.1540-8175.2007.00505.x.
3
Effusive--constrictive epicarditis that developed more than 5 years after ventricular septal defect closure: two cases relieved by epicardiectomy.
室间隔缺损闭合术后5年以上发生的渗出性缩窄性心包炎:两例经心包切除术缓解
Pediatr Cardiol. 2005 Nov-Dec;26(6):872-6. doi: 10.1007/s00246-005-0990-8.
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Effusive-constrictive pericarditis.渗出性缩窄性心包炎
N Engl J Med. 2004 May 27;350(22):2310-2; author reply 2310-2.
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Severe heart failure due to subacute effusive-constrictive pericarditis in a child.一名儿童因亚急性渗出性缩窄性心包炎导致严重心力衰竭。
Pediatr Cardiol. 2005 Jan-Feb;26(1):101-3. doi: 10.1007/s00246-003-0697-7.
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N Engl J Med. 2004 Jan 29;350(5):435-7. doi: 10.1056/NEJMp038199.
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