Chen Meng-Yu, Chen Yih-Sharng, Chen Shyh-Jye, Lu Chun-Wei
Department of Pediatrics, National Taiwan University Hospital, No 8, Chung-San South Road, Taipei 100, Taiwan.
Pediatr Cardiol. 2011 Jun;32(5):681-4. doi: 10.1007/s00246-011-9927-6. Epub 2011 Feb 27.
Effusive-constrictive pericarditis is characterized by constriction of visceral pericardium with a coexisting tense pericardial effusion. We report a 10-year-old girl with right heart failure due to effusive-constrictive pericarditis. She did not present typical features, such as cardiac tamponade or thickening of pericardium (visceral and parietal), but constrictive physiology was observed by echocardiography and cardiac computed tomography. These noninvasive imaging modalities provided clinical clues to make precise diagnosis. The patient underwent surgical drainage of pericardial fluid and visceral pericardiectomy, which resulted in improved hemodynamics and symptoms.
渗出-缩窄性心包炎的特征是脏层心包缩窄并伴有同时存在的大量心包积液。我们报告了一名10岁因渗出-缩窄性心包炎导致右心衰竭的女孩。她未表现出典型特征,如心脏压塞或心包(脏层和壁层)增厚,但超声心动图和心脏计算机断层扫描观察到缩窄性生理改变。这些非侵入性成像方式为做出准确诊断提供了临床线索。患者接受了心包积液手术引流和脏层心包切除术,血流动力学和症状均得到改善。