Albuquerque Lígia Guedes Morais de, França Emmanuel Rodrigues de, Kozmhinsky Valter, Querino Marina Coutinho Domingues, Morais Amanda Guedes de
Prof. Emmanuel Franca Dermatology Clinic, Recife, PE, Brazil.
An Bras Dermatol. 2011 Jan-Feb;86(1):131-4. doi: 10.1590/s0365-05962011000100019.
Erythromelalgia is a rare clinical syndrome characterized by heat, redness and intermittent pain in the extremities, being most frequent the bilateral development in the lower extremities. Local cooling brings relief to symptoms, while heating, physical exercises and use of stockings/socks intensify the discomfort. This condition can be primary or idiopathic or secondary to haematological disorders and vascular inflammatory and degenerative diseases. It is reported the case of an eighteen-year-old male who presented, at the early age of two, development of the symptoms of erythema ,heat and pain followed by desquamation of hands and feet, in outbreaks, with intervals 4 to 5 years long between the crises.
红斑性肢痛症是一种罕见的临床综合征，其特征为四肢发热、发红和间歇性疼痛，最常见于双下肢。局部降温可缓解症状，而加热、体育锻炼和穿长袜/短袜会加重不适感。这种情况可以是原发性或特发性的，也可以是继发于血液系统疾病以及血管炎性和退行性疾病。报告了一例18岁男性病例，该患者在两岁时就开始出现红斑、发热和疼痛症状，随后手脚出现脱屑，呈发作性，发作间期长达4至5年。
