Kahrom Mahdi, Kahrom Hadi
Division of Cardiothoracic Surgery, Imam Reza Hospital, Mashhad University of Medical Sciences, Mashhad, Iran.
Pan Afr Med J. 2009 Dec 17;3:20.
The Scimitar syndrome is a rare congenital anomaly that consists in part of total or partial anomalous venous drainage of the right lung to the inferior vena cava (IVC). This descending vein is visible on CXR as a curvilinear density along the right heart border and resembles the curved Turkish sword that gives the condition its name. Scimitar syndrome forms part of the large spectrum of associated conditions known as venolobar syndrome. These include right lung hypoplasia or sequestered segments of the right lung, congenital heart disease and various others. Surgical approaches to the Scimitar syndrome have varied according to the anatomic and pathologic features presented in each case. Here we review the clinical signs and symptoms, diagnostic dilemmas, current medical and surgical managements of Scimitar syndrome.
弯刀综合征是一种罕见的先天性异常，部分表现为右肺全部或部分静脉血异常引流至下腔静脉。这条下行静脉在胸部X线片上表现为沿右心缘的曲线状致密影，形似弯曲的土耳其弯刀，该病即因此得名。弯刀综合征是静脉叶综合征这一广泛相关病症谱的一部分。这些病症包括右肺发育不全或右肺隔离肺段、先天性心脏病及其他各种疾病。针对弯刀综合征的手术方法因每个病例呈现的解剖和病理特征而异。在此，我们综述弯刀综合征的临床体征和症状、诊断难题以及当前的内科和外科治疗方法。
