Dasari Nikhila, Valapala Venkat Narayana Goutham, Anim Roopa
Department of Respiratory Medicine, GITAM Institute of Medical Sciences and Research, GITAM (Deemed to be University), Rushikonda, Visakhapatnam, Andhra Pradesh, India.
Department of General Medicine, GITAM Institute of Medical Sciences and Research, GITAM (Deemed to be University), Rushikonda, Visakhapatnam, 530045, Andhra Pradesh, India.
Radiol Case Rep. 2022 Apr 20;17(6):2231-2234. doi: 10.1016/j.radcr.2022.03.077. eCollection 2022 Jun.
Scimitar syndrome is a rare congenital anomaly which is characterised by anomalous pulmonary venous drainage of the either entire right lung or part of it into the inferior vena cava or portal vein or hepatic vein or right atrium occasionally. This can be associated with hypoplasia of the right lung, dextroposition, underdevelopment of right pulmonary artery and anomalous systemic arterial supply from the descending aorta to the hypoplastic lung. A 36 year old female came with history of swelling in the right breast which turned up to be right breast fibroadenoma. Routine chest radiograph revealed scimitar syndrome which was confirmed on CECT chest.
弯刀综合征是一种罕见的先天性异常,其特征是整个右肺或部分右肺的肺静脉异常引流至下腔静脉、门静脉、肝静脉,偶尔引流至右心房。这可能与右肺发育不全、右旋、右肺动脉发育不良以及降主动脉向发育不全的肺提供异常体循环动脉供血有关。一名36岁女性因右乳肿胀前来就诊,结果发现是右乳纤维腺瘤。常规胸部X线片显示弯刀综合征,胸部CT血管造影证实了这一诊断。