Panesar Gurpreet, Bhende Vishal V, Sharma Tanishq S, Patel Nirja, Kumar Amit, Trivedi Bhadra Y, Soni Kunal, Dhami Kartik, Mehta Deepakkumar V
Cardiac Anaesthesiology, Bhanubhai and Madhuben Patel Cardiac Centre, Shree Krishna Hospital, Anand, IND.
Pediatric Cardiac Surgery, Bhanubhai and Madhuben Patel Cardiac Centre, Shree Krishna Hospital, Anand, IND.
Cureus. 2021 Oct 28;13(10):e19107. doi: 10.7759/cureus.19107. eCollection 2021 Oct.
The low prevalence of scimitar syndrome along with its varied clinical presentation poses a diagnostic dilemma to the treating clinicians. It usually falls under a large spectrum of conditions called venolobar syndrome. Scimitar involves the partial venous drainage of the right lung to the inferior vena cava (IVC). We share our experience of two cases that were diagnosed as partial anomalous pulmonary venous connection/drainage (PAPVC/PAPVD) on echocardiography but CT scan revealed the underlying scimitar syndrome. Perioperative pulmonary arterial hypertension, intraoperative ventilation strategies for managing associated lung hypoplasia, and postoperative right ventricular dysfunction are a few challenges faced in the perioperative period.
弯刀综合征的低发病率及其多样的临床表现给临床治疗医生带来了诊断难题。它通常属于一大类称为肺静脉叶综合征的病症。弯刀综合征涉及右肺部分静脉血引流至下腔静脉。我们分享两例病例的经验，这两例病例在超声心动图检查中被诊断为部分性肺静脉异位连接/引流（PAPVC/PAPVD），但CT扫描显示其潜在的弯刀综合征。围手术期肺动脉高压、处理相关肺发育不全的术中通气策略以及术后右心室功能障碍是围手术期面临的一些挑战。
