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一名54岁男性出现双侧肺泡浸润及前列腺肿瘤。

Bilateral pulmonary alveolar infiltrate and prostate tumour in a 54-year-old man.

作者信息

Figueiredo André A, Brandao Guilherme, Dentz Leonardo C, Alves Christiane M M, Stroppa Antonio E S

机构信息

Universidade Federal de Juiz de Fora, Morphology and Urology, Rua Irineu Marinho 365 Apto 801 - Bloco 3, Bom Pastor, Juiz de Fora MG, CEP 36021-58, Brazil.

出版信息

BMJ Case Rep. 2009;2009. doi: 10.1136/bcr.09.2008.0888. Epub 2009 Feb 2.

DOI:10.1136/bcr.09.2008.0888
PMID:21686581
原文链接:https://pmc.ncbi.nlm.nih.gov/articles/PMC3030294/
Abstract

THIS CASE STUDY DESCRIBES THE ASSOCIATION BETWEEN TWO RARE ENTITIES

pulmonary alveolar proteinosis (PAP) and embryonic rhabdomyosarcoma of the prostate in a 54 year old male presenting with pulmonary symptoms and obstructive urinary symptoms. The prostate tumour was treated with a radical cystectomy and adjuvant chemotherapy and radiotherapy. The patient did not wish to have treatment for his pulmonary disease and died 1 year after surgery as a result of intra-abdominal spread of the neoplasm.

摘要

本病例研究描述了两个罕见病症之间的关联

肺泡蛋白沉积症(PAP)和一名54岁男性的前列腺胚胎性横纹肌肉瘤,该患者同时出现肺部症状和尿路梗阻症状。前列腺肿瘤接受了根治性膀胱切除术及辅助化疗和放疗。患者不希望对其肺部疾病进行治疗,术后1年因肿瘤腹腔内扩散而死亡。

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本文引用的文献

1
GM-CSF autoantibodies and neutrophil dysfunction in pulmonary alveolar proteinosis.肺泡蛋白沉积症中的粒细胞-巨噬细胞集落刺激因子自身抗体与中性粒细胞功能障碍
N Engl J Med. 2007 Feb 8;356(6):567-79. doi: 10.1056/NEJMoa062505.
2
Pulmonary alveolar proteinosis. Clinical manifestations and optimal treatment strategies.肺泡蛋白沉积症。临床表现及最佳治疗策略。
Treat Respir Med. 2004;3(4):217-27. doi: 10.2165/00151829-200403040-00002.
3
Adult prostate sarcoma: the M. D. Anderson Cancer Center Experience.成人前列腺肉瘤:MD安德森癌症中心的经验
J Urol. 2001 Aug;166(2):521-5. doi: 10.1016/s0022-5347(05)65974-5.
4
Pulmonary alveolar proteinosis: clinical features and outcomes.肺泡蛋白沉积症:临床特征与转归
Chest. 1998 Nov;114(5):1357-62. doi: 10.1378/chest.114.5.1357.
5
Pulmonary alveolar proteinosis. Occurrence with metastatic melanoma to lung.肺泡蛋白沉积症。合并肺转移性黑色素瘤。
Chest. 1989 Feb;95(2):466-7. doi: 10.1378/chest.95.2.466.