Liang R, Woo E, Ho F, Collins R, Choy D, Ma J
University Department of Medicine, Queen Mary Hospital, Hong Kong.
Med Pediatr Oncol. 1990;18(3):236-9. doi: 10.1002/mpo.2950180316.
Klinefelter's syndrome is known to be associated with various malignancies including male breast cancer and germ cell tumour. We report a patient with Klinefelter's syndrome who developed a primary B-cell lymphoma of the central nervous system (CNS). To the best of our knowledge, this is the first case of primary CNS lymphoma in Klinefelter's syndrome.