Department of Oral Diagnosis - Oral Semiology and Oral Pathology Sections, Piracicaba Dental School - State University of Campinas, Piracicaba, Sao Paulo, Brazil.
J Oral Pathol Med. 2012 Feb;41(2):178-85. doi: 10.1111/j.1600-0714.2011.01073.x. Epub 2011 Aug 29.
Amyloidosis is associated with or caused by amyloid deposition. These fibrillar proteins may be deposited extracellularly causing tissue damage or impairment.
The aim of the study was to retrospectively review pathology archives in two oral diagnostic centers for cases fulfilling criteria of amyloidosis and to differentiate AA and AL types of amyloidosis.
The clinicopathological features, alkaline Congo red staining, with and without pretreatment with potassium permanganate, and immunohistochemical (IHC) staining with anti-AA, anti-kappa (κ), and anti-lambda (λ) light chain antibodies were carried out and analyzed.
The search identified 14 cases. Ten patients were women and four were men, with a mean age of 58 years. Eleven patients had systemic involvement by amyloidosis (associated either with multiple myeloma or plasma cell dyscrasia/monoclonal gammopathies), while three presented the localized type, one of them associated with plasmacytoma. All cases showed positivity for κ or λ light chains (AL-amyloid) and presented resistance to the potassium permanganate pretreatment.
Our results show that the head and neck region is preferentially affected by systemic AL-amyloidosis, usually associated with plasma cell dyscrasia. Interestingly, two cases affected by inflammatory rheumatic diseases presented AL-amyloid deposition. Moreover, even after pretreatment with potassium permanganate, which was helpful in highlighting the presence of AL-amyloid, in agreement with the IHC findings, clinical classifications should be carefully made in systemic amyloidosis.
淀粉样变性与淀粉样物质沉积有关或由其引起。这些纤维状蛋白可能沉积于细胞外,导致组织损伤或功能障碍。
本研究旨在回顾两个口腔诊断中心的病理档案,以寻找符合淀粉样变性标准的病例,并对 AA 型和 AL 型淀粉样变性进行区分。
对临床病理特征、碱性刚果红染色(直接法和高锰酸钾预处理法)及抗 AA、抗 κ(κ)和抗 λ(λ)轻链抗体免疫组化染色进行分析。
共发现 14 例病例。10 例为女性,4 例为男性,平均年龄 58 岁。11 例患者存在全身性淀粉样变性(与多发性骨髓瘤或浆细胞异常/单克隆丙种球蛋白病相关),3 例为局限性淀粉样变性,其中 1 例与浆细胞瘤相关。所有病例均对 κ 或 λ 轻链呈阳性(AL 淀粉样变性),且对高锰酸钾预处理具有抗性。
我们的研究结果表明,头颈部是系统性 AL 淀粉样变性的好发部位,通常与浆细胞异常有关。有趣的是,有两例炎症性风湿性疾病患者出现 AL 淀粉样物质沉积。此外,即使在经过高锰酸钾预处理后(该预处理有助于突出 AL 淀粉样变性的存在,与免疫组化结果一致),对于系统性淀粉样变性,仍应仔细进行临床分类。